Fatal cerebellar herniation secondary to Camurati-Englemann's disease.

Fatal cerebellar herniation secondary to Camurati-Englemann's disease.

Suboccipital craniotomy and cervical laminectomy were performed in a patient with Camurati-Englemann's disease to relieve symptoms of medullary compression. In spite of surgical decompression, the patient expired on the fourth postoperative day from cerebellar herniation.

[Camurati-Engelmann disease].

1Senior Registrar, Endocrinology, 2Consultant Endocrinologist, 3Consultant Radiologist, 4Senior Registrar, Orthopedic, 5Consultant Orthopedic Surgeon, 6Consultant Histo Pathologist, National Hospital of Sri Lanka. Figure 1. Xray skull – lateral. Figure 2. Histology of the bone biopsy shows mature thick cortical lamellar bone with regular prominent cement lines (thick arrow) with prominent osteo...

Regarding Camurati-Engelmann Disease: To the Editor

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